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Детская хирургия. Журнал им. Ю.Ф. Исакова. 2022; 26: 47-50

Лапароскопическое лечение дуоденальной атрезии, ассоциированной с situs inversus abdominis у новорождённой

Щербинин Р. Л., Добродомова С. В., Вечеркин В. А., Хорошилов Д. О., Бочарова Н. В., Дроздов С. И., Крюков Ю. В.

https://doi.org/10.55308/1560-9510-2022-26-1-47-50

Аннотация

Введение. Сочетание врождённой дуоденальной атрезии (ДА) с situs inversus abdominis (SIA) встречается крайне редко. В исследовании представлено описание использования лапароскопии для лечения этой ассоциации.
Описание клинического наблюдения. Новорождённая девочка была доставлена в клинику БУЗ ВО «Воронежская областная детская клиническая больница № 1» на 4-е сутки жизни с регулярной рвотой желчью и потерей массы тела. В результате обследования у ребёнка выявлена ДА в сочетании с SIA. После предоперационной подготовки ребёнку выполнен дуоденодуоденоанастомоз по Kimura. В результате проведённого лечения проходимость двенадцатиперстной кишки (ДПК) восстановлена. Ребёнок выписан в удовлетворительном состоянии на полном энтеральном питании с хорошей динамикой набора массы тела.
Заключение. Представленный случай демонстрирует возможность успешного лапароскопического лечения врождённой дуоденальной обструкции в сочетании с SIA в условиях профильного стационара 3-го уровня.

Список литературы

1. AlKhlaiwy O., AlMuhsin A.M., Zakarneh E., et al. Laparoscopic cholecystectomy in situs inversus totalis: case report with review of techniques. Int J Surg Case Rep. 2019; 59: 208–12.

2. Nawaz A., Matta H., Hamchou M., et al. Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature. Pediatr Surg Int. 2005; 21: 589–92.

3. Qiang S., Fan M., Cui Q., Li Z., Zhou Y., Li Q., Li F. Management of duodenal atresia associated with situs inversus abdominus: a case report. Medicine. 2020; 99: 31.

4. Rahul Gupta, Varsha Soni, Prakash Devidas Valse, Ram Babu Goyal, Arun Kumar Gupta, Praveen Mathur Neonatal intestinal obstruction associated with situs inversus totalis: two case reports and a review of the literature. J Med Case Rep. 2017; 11: 264.

5. Козлов Ю.А., Новожилов В.А., Распутин А.А., Сыркин Н.В., Подкаменев А.В., Юрков П.С., Соловьев А.А., Вебер И.Н., Кононенко М.И. Лапароскопическая дуоденодуоденостомия в лечении врождённой дуоденальной непроходимости – первоначальный опыт. Детская хирургия. 2012; 5: 34–7. Kozlov Yu.A., Novozhilov V.A., Rasputin A.A., Syrkin N.V., Podkamenev A.V., Yurkov P.S., Soloviev A.A., Weber I.N., Kononenko M.I. Laparoscopic duodenoduodenostomy in the management of congenital duodenal obstruction – first experience. Detskaya Khirurgiya. 2012; 5: 34–7. (In Russian)

6. Козлов Ю.А., Новожилов В.А., Тысячный А.С., Кононенко М.И., Кузнецова Н.Н. Сравнительный анализ использования лапаротомии и лапароскопии в лечении дуоденальной атрезии. Анналы хирургии. 2013; 4: 26–34. Kozlov Yu.A., Novozhilov V.A., Tysyachnyy A.S., Kononenko M.I., Kuznetsova N.N. Comparative analysis of the laparotomy and laparoscopy in the treatment of duodenal atresia. Annaly Khirurgii. 2013; 4: 26–34. (In Russian)

7. Choudhry M.S., Rahman N., Boyd P., et al. Duodenal atresia: associated anomalies, prenatal diagnosis and outcome. Pediatr Surg Int. 2009; 25: 727–30.

8. Bishop J.C., McCormick B., Johnson C.T., et al. The double bubble sign: duodenal atresia and associated genetic etiologies. Fetal Diagn Ther 2020; 47: 98–103.

9. Van der Zee D.C. Laparoscopic repair of duodenal atresia: revisited. World J Surg. 2011; 35: 1781–4.

10. Adams S.D., Stanton M.P. Malrotation and intestinal atresias. Early Hum Dev. 2014; 90: 921–5.

11. Gharpure V. Duodenal atresia. J Neonatal Surg. 2014; 3: 14.

12. Jones M.L.M., Sarila G., Chapuis P., et al. The role of fibroblast growth factor 10 signaling in duodenal atresia. Front Pharmacol. 2020; 11: 250.

13. Brantberg A., Blaas H.G., Salvesen K.A., et al. Fetal duodenal obstructions: increased risk of prenatal sudden death. Ultrasound Obstet Gynecol. 2002; 20: 439–46.

Russian Journal of Pediatric Surgery. 2022; 26: 47-50

Laparoscopic treatment of duodenal atresia associated with situs inversus abdominis in a newborn

Shcherbinin R. L., Dobrodomova S. V., Vecherkin V. A., Khoroshilov D. O., Bocharova N. V., Drozdov S. I., Kryukov Yu. V.

https://doi.org/10.55308/1560-9510-2022-26-1-47-50

Abstract

Introduction. A combination of congenital duodenal obstruction (CDO) and situs inversus abdominis (SIA) is an extremely rare case. The present article describes a laparoscopic technique applied for the care in such patient.
Case presentation. A newborn girl was admitted to the hospital on the 4th day of her life with regular bile vomiting and weight loss. Examination revealed CDO combined with SIA. After preoperative preparation and condition stabilization, the child was operated on and Kimura duodenoduodenoanastomosis was put. After the performed treatment, duodenal patency was restored. The patient was discharged home in a satisfactory state. She had complete enteral feeding with a good dynamics of weight gain.
Conclusion. The described case demonstrates the effectiveness of laparoscopic approach in patients with CDO and SIA hospitalized in a regional children`s hospital.

References

1. AlKhlaiwy O., AlMuhsin A.M., Zakarneh E., et al. Laparoscopic cholecystectomy in situs inversus totalis: case report with review of techniques. Int J Surg Case Rep. 2019; 59: 208–12.

2. Nawaz A., Matta H., Hamchou M., et al. Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature. Pediatr Surg Int. 2005; 21: 589–92.

3. Qiang S., Fan M., Cui Q., Li Z., Zhou Y., Li Q., Li F. Management of duodenal atresia associated with situs inversus abdominus: a case report. Medicine. 2020; 99: 31.

4. Rahul Gupta, Varsha Soni, Prakash Devidas Valse, Ram Babu Goyal, Arun Kumar Gupta, Praveen Mathur Neonatal intestinal obstruction associated with situs inversus totalis: two case reports and a review of the literature. J Med Case Rep. 2017; 11: 264.

5. Kozlov Yu.A., Novozhilov V.A., Rasputin A.A., Syrkin N.V., Podkamenev A.V., Yurkov P.S., Solov'ev A.A., Veber I.N., Kononenko M.I. Laparoskopicheskaya duodenoduodenostomiya v lechenii vrozhdennoi duodenal'noi neprokhodimosti – pervonachal'nyi opyt. Detskaya khirurgiya. 2012; 5: 34–7. Kozlov Yu.A., Novozhilov V.A., Rasputin A.A., Syrkin N.V., Podkamenev A.V., Yurkov P.S., Soloviev A.A., Weber I.N., Kononenko M.I. Laparoscopic duodenoduodenostomy in the management of congenital duodenal obstruction – first experience. Detskaya Khirurgiya. 2012; 5: 34–7. (In Russian)

6. Kozlov Yu.A., Novozhilov V.A., Tysyachnyi A.S., Kononenko M.I., Kuznetsova N.N. Sravnitel'nyi analiz ispol'zovaniya laparotomii i laparoskopii v lechenii duodenal'noi atrezii. Annaly khirurgii. 2013; 4: 26–34. Kozlov Yu.A., Novozhilov V.A., Tysyachnyy A.S., Kononenko M.I., Kuznetsova N.N. Comparative analysis of the laparotomy and laparoscopy in the treatment of duodenal atresia. Annaly Khirurgii. 2013; 4: 26–34. (In Russian)

7. Choudhry M.S., Rahman N., Boyd P., et al. Duodenal atresia: associated anomalies, prenatal diagnosis and outcome. Pediatr Surg Int. 2009; 25: 727–30.

8. Bishop J.C., McCormick B., Johnson C.T., et al. The double bubble sign: duodenal atresia and associated genetic etiologies. Fetal Diagn Ther 2020; 47: 98–103.

9. Van der Zee D.C. Laparoscopic repair of duodenal atresia: revisited. World J Surg. 2011; 35: 1781–4.

10. Adams S.D., Stanton M.P. Malrotation and intestinal atresias. Early Hum Dev. 2014; 90: 921–5.

11. Gharpure V. Duodenal atresia. J Neonatal Surg. 2014; 3: 14.

12. Jones M.L.M., Sarila G., Chapuis P., et al. The role of fibroblast growth factor 10 signaling in duodenal atresia. Front Pharmacol. 2020; 11: 250.

13. Brantberg A., Blaas H.G., Salvesen K.A., et al. Fetal duodenal obstructions: increased risk of prenatal sudden death. Ultrasound Obstet Gynecol. 2002; 20: 439–46.