Российский вестник детской хирургии, анестезиологии и реаниматологии. 2016; 6: 37-42
ПЕРСИСТИРУЮЩАЯ КЛОАКА У ДЕВОЧЕК. ПРОБЛЕМЫ ДИАГНОСТИКИ И ХИРУРГИЧЕСКОЙ КОРРЕКЦИИ
Аннотация
В статье представлен краткий обзор литературных данных о персистирующей клоаке, а также результаты диагностики и лечения 16 девочек с указанной патологией в нашей клинике. ПК представляет собой многовариантное слияние анатомических структур с формированием общего канала или урогенитального синуса. Это обуславливает возникновение различных осложнений, требующих оперативного вмешательства. С протяженностью общего канала увеличивается число сопутствующих аномалий с выраженными анатомическими и функциональными нарушениями. В 4 наблюдениях оперативные вмешательства проведены без наложения колостомы, в 12 – с колостомой. Метод выбора хирургической коррекции – заднесагиттальная аноректоуретеровагинопластика. В трех наблюдениях дополнительно использован брюшно-промежностный доступ.
Список литературы
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Russian Journal of Pediatric Surgery, Anesthesia and Intensive Care. 2016; 6: 37-42
PERSISTING CLOACA IN GIRLS. THE ISSUES OF DIAGNOSTICS AND SURGICAL CORRECTION
Abstract
The article presents the summary of literature data on the persistent cloaca, results of diagnostics and treatment of 16 girls with the mentioned pathology at our clinic. The PC is a multivariant fusion of anatomical structures forming the common canal or urogenital sinus. This explains occurrence of different complications requiring surgeries. The number of concurrent abnormalities with pronounced anatomical and functional disturbances is increased alongside with the length of the common canal. In 4 observations surgeries were performed without colostomy and in 12 cases these were done applying colostomy. Posterior and sagittal anorecto-ureterovaginoplasty procedure was the method of choice for surgical correction. The abdominoperineal approach was used in 3 observations as an addition.
References
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2. Hendren WH. Cloaca, the most severe degree of imperforate anus// Ann Surg 1998. – vol. 228, N 3. – pp. 331–346.
3. Krstic ZD, Lukac M, Lukac R, et al. Surgical treatment of cloacal anomalies// Pediatr Surg Int. 2001. – vol. 17. – pp. 329–333.
4. Bischoff A., Levvit M. A., Lim F. Y., Guimaraes C., Alberto P. Prenatal diagnosis of cloacal malformations// J. Pediatric Surgery Int., 2010. – Vol. 26. – pp. 1071–1075.
5. Bischoff A., Calvo-Garcia M. A., Baregamian N.,Levvit M. A., Lim F. Y., et all. Prenatal counseling for cloaca and cloacal exstrophy-challenges faced by pediatric surgeons// J. Pediatr Surg. Int., 2012. – Vol.28. – pp.781–788.
6. Chitrit Y., Vuillard E., Khung S., Belarbi N., Guimiot F. et all. Cloaca in Discordant Monoamniotic Twins: Prenatal Diagnosis and Consequence for Fetal Lung Development //Am J Perinatol Rep. 2014. Vol.4. – pp. 33–36.
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