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4. Tangye S.G., Al-Herz W., Bousfiha A., et al. Human Inborn Errors of Immunity: 2019 Update on the Classification from the International Union of Immunological Societies Expert Committee [published correction appears in J Clin Immunol 2020; 40 (1): 24– 64.

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15. Wanat K.A., Elenitsas R., Kim E.J., Rosenbach M. Granuloma annulare associated with cutaneous marginal zone lymphoma: a case linking a hematologic malignancy with granulomatous dermatitis. Am J Dermatopathol 2012; 34 (8): 844–6.

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1. Immunologiya detskogo vozrasta. Prakticheskoe rukovodstvo po detskim boleznyam. Pod red. Shcherbiny A.Yu., Pashanova E.D. M.: Medpraktika-M; 2006.

2. Picard C., Bobby Gaspar H., Al-Herz W., et al. International Union of Immunological Societies: 2017 primary immunodeficiency diseases committee report on inborn errors of immunity. J Clin Immunol 2018; 38 (1): 96–128.

3. Bousfiha A., Jeddane L., Picard C., et al. Human Inborn Errors of Immunity: 2019 Update of the IUIS Phenotypical Classification. J Clin Immunol 2020; 40 (1): 66–81.

4. Tangye S.G., Al-Herz W., Bousfiha A., et al. Human Inborn Errors of Immunity: 2019 Update on the Classification from the International Union of Immunological Societies Expert Committee [published correction appears in J Clin Immunol 2020; 40 (1): 24– 64.

5. Bousfiha A., Jeddane L., Picard C., et al. The 2017 IUIS Phenotypic Classification for Primary Immunodeficiencies. J Clin Immunol 2018; 38 (1): 129–43. DOI:10.1007/s10875-017-0465-8

6. Sharma D., Jindal A.K., Rawat A., Singh S. Approach to a Child with Primary Immunodeficiency Made Simple. Indian Dermatol Online J 2017; 8 (6): 391–405.

7. Kuzmenko N.B., Shcherbina A.Y. Classification of primary immunodeficiencies as a reflection of modern ideas about their pathogenesis and therapeutic approaches. Russian Journal of Pediatric Hematology and Oncology. 2017; 4 (3): 51–7. (In Russ.).

8. Produktivnoe vospalenie. Rukovodstvo dlya vrachei. Pod red. Povzun S.A. S.-Pb.: spetsLit; 2018. 359 s.

9. Elbaz T., Esmat G. Hepatic and intestinal schistosomiasis: review. J Adv Res 2013; 4: 445–52.

10. Wilson M.S., Mentink-Kane M.M., Pesce J.T., Ramalingam T.R., Thompson R., Wynn T.A. Immunopathology of schistosomiasis. Immunol Cell Biol 2007; 85: 148–54.

11. Martín-Callizo C., Marcoval J., Penín R.M. Granulomatous Reactions to Red Tattoo Pigments: A Description of 5 Cases. Actas Dermosifiliogr 2015; 106 (7): 588–90.

12. Molina-Ruiz A.M., Requena L. Foreign body granulomas. Dermatol Clin 2015; 33 (3): 497–523.

13. Piette E.W., Rosenbach M. Granuloma annulare: pathogenesis, disease associations and triggers, and therapeutic options. J Am Acad Dermatol 2016; 75 (3): 467–79.

14. Mangold A.R., Cumsky H.J.L., Costello C.M., et al. Clinical and histopathologic features of paraneoplastic granuloma annulare in association with solid organ malignancies: A case-control study. J Am Acad Dermatol 2018; 79 (5): 913–20.e1.

15. Wanat K.A., Elenitsas R., Kim E.J., Rosenbach M. Granuloma annulare associated with cutaneous marginal zone lymphoma: a case linking a hematologic malignancy with granulomatous dermatitis. Am J Dermatopathol 2012; 34 (8): 844–6.

16. Valeyre D., Prasse A., Nunes H., et al. Sarcoidosis. Lancet 2014; 383: 1155–67.

17. Caso F., Galozzi P., Costa L., Sfriso P., Cantarini L., Punzi L. Autoinflammatory granulomatous diseases: from Blau syndrome and early-onset sarcoidosis to NOD2-mediated disease and Crohn's disease. RMD Open 2015; 1 (1): e000097.

18. Lo Schiavo A., Ruocco E., Gambardella A., O’Leary R.E., Gee S. Granulomatous dysimmune reactions (sarcoidosis, granuloma annulare, and others) on differently injured skin areas. Clin Dermatol 2014; 32 (5): 646–53.

19. Chua-Aguilera C.J., Möller B., Yawalkar N. Skin manifestations of rheumatoid arthritis, juvenile idiopathic arthritis, and spondyloarthritides. Clin Rev Allergy Immunol 2017; 53 (3): 371–93.

20. Fischer A., Provot J., Jais J.P., et al.; members of the CEREDIH French PID study group. Autoimmune and inflammatory manifestations occur frequently in patients with primary immunodeficiencies. J Allergy Clin Immunol 2017; 140 (5): 1388–93.e8.

21. Schuetz C., Huck K., Gudowius S., et al. An immunodeficiency disease with RAG mutations and granulomas. N Engl J Med 2008; 358: 2030–38

22. ESID Registry – Working Definitions for Clinical Diagnosis of PID https://esid.org/content/download/13053/372959/file/ESIDRegistry_ClinicalCriteria2014.pdf (accessed December 15, 2019)

23. Asai J. What is new in the histogenesis of granulomatous skin diseases? J Dermatol 2017; 44 (3): 297–303.

24. Terziroli Beretta-Piccoli B., Mainetti C., Peeters M. et al. Cutaneous Granulomatosis: a Comprehensive Review. Clinic Rev Allerg Immunol 2018; 54: 131–46.

25. Wilson J.L., Mayr H.K., Weichhart T. Metabolic Programming of Macrophages: Implications in the Pathogenesis of Granulomatous Disease. Front Immunol 2019; 10: 2265.

26. Girgis N.M., Gundra U.M., Ward L.N., et al. Ly6C(high) monocytes become alternatively activated macrophages in schistosome granulomas with help from CD4+ cells. PLoS Pathog 2014; 10: e1004080.

27. Silva D.A.A.D., Silva M.V.D., Barros C.C.O., et al. TNF-a blockade impairs in vitro tuberculous granuloma formation and down modulate Th1, Th17 and Treg cytokines. PLoS One 2018; 13 (3): e0194430.

28. Boros D.L. New perspectives on ancient granulomas. Front Immunol 2013; 4: 345. DOI: 10.3389/fimmu.2013.00345

29. Li X., Körner H., Liu X. Susceptibility to Intracellular Infections: Contributions of TNF to Immune Defense. Front Microbiol 2020; 11: 1643.

30. Timmermans W.M., van Laar J.A., van Hagen P.M., van Zelm M.C. Immunopathogenesis of granulomas in chronic autoinflammatory diseases. Clin Transl Immunol 2016; 5 (12): e118.

31. Huang Z., Luo Q., Guo Y., et al. Mycobacterium tuberculosis- induced polarization of human macrophage orchestrates the formation and development of tuberculous granulomas in vitro. PLoS ONE 2015; 10: e0129744.

32. Essandoh K., Li Y., Huo J., Fan G.C. MiRNA-Mediated Macrophage Polarization and its Potential Role in the Regulation of

33. Inflammatory Response. Shock 2016; 46 (2): 122–31.

34. Jetten N., Roumans N., Gijbels M.J., et al. Wound administration of M2-polarized macrophages does not improve murine cutaneous healing responses. PLoS One 2014; 9 (7): e102994.

35. Kumar R., Singh P., Kolloli A., et al. Immunometabolism of Phagocytes During Mycobacterium tuberculosis Infection. Front Mol Biosci 2019; 6: 105.

36. Wojtan P., Mierzejewski M., Osinska I., Domagala-Kulawik J. Macrophage polarization in interstitial lung diseases. Cent Eur J Immunol 2016; 41: 159–64.

37. Mattila J.T., Ojo O.O., Kepka-Lenhart D., et al. Microenvironments in tuberculous granulomas are delineated by distinct populations of macrophage subsets and expression of nitric oxide synthase and arginase isoforms. J Immunol 2013; 191:

38. –84.

39. Khan A., Singh V.K., Hunter R.L., Jagannath C. Macrophage heterogeneity and plasticity in tuberculosis. J Leukoc Biol 2019; 106 (2): 275–82.

40. Terziroli Beretta-Piccoli B., Mainetti C., Peeters M., et al. Cutaneous Granulomatosis: a Comprehensive Review. Clinic Rev Allerg Immunol 2018; 54: 131–46.

41. Wick MR. Granulomatous & histiocytic dermatitides. Semin Diagn Pathol. 2017;34(3):301-311.

42. Ito T., Connett J.M., Kunkel S.L., Matsukawa A. The linkage of innate and adaptive immune response during granulomatous development. Front Immunol 2015; 4: 10.

43. Norouzi S., Aghamohammadi A., Mamishi S., et al. Bacillus Calmette-Guérin (BCG) complications associated with primary immunodeficiency diseases. J Infect 2012; 64 (6): 543–54.

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